An important role of heparan sulfate proteoglycan (Perlecan) in a model system for the deposition and persistence of fibrillar A beta-amyloid in rat brain

Neuron. 1994 Jan;12(1):219-34. doi: 10.1016/0896-6273(94)90165-1.

Abstract

A consistent rat model for the study of the consequences of congophilic and fibrillar A beta-amyloid in brain has been developed. One hundred percent of animals receiving infusions of synthetic beta-amyloid protein (A beta 1-40) plus a specific heparan sulfate proteoglycan (HSPG) for 1 week or 7 weeks (following 2 week infusions) demonstrated Congo red and thioflavin S-positive deposits adjacent to the infusion site. Extracellular amyloid fibrils were identified by electron microscopy and were immunogold decorated with A beta antibody. Significant increases in Congo red staining were observed in animals infused with A beta plus HSPG versus those infused with only A beta. Infusion of A beta alone was variable with respect to congophilic amyloid persistence, which occurred in 50% of animals and only when endogenous HSPGs accumulated at A beta deposition sites. By 7 weeks, only animals infused with A beta plus HSPG demonstrated compaction of the Congo red material from amorphous, wispy deposits (at 1 week) to stellate deposits resembling a Maltese cross. These spherical amyloid deposits were very similar to Congo red-stained amyloid plaques in human Alzheimer's disease brain, and in vitro data suggest that they were probably formed in vivo following interactions with endogenous brain components.

Publication types

  • Research Support, Non-U.S. Gov't
  • Research Support, U.S. Gov't, P.H.S.

MeSH terms

  • Amyloid beta-Peptides / administration & dosage
  • Amyloid beta-Peptides / metabolism*
  • Animals
  • Benzothiazoles
  • Brain / metabolism*
  • Brain / ultrastructure
  • Congo Red
  • Glycosaminoglycans / analysis
  • Glycosaminoglycans / metabolism
  • Heparan Sulfate Proteoglycans
  • Heparitin Sulfate / administration & dosage
  • Heparitin Sulfate / isolation & purification
  • Heparitin Sulfate / metabolism*
  • Immunohistochemistry
  • Infusions, Parenteral
  • Male
  • Mice
  • Microscopy, Electron
  • Microscopy, Immunoelectron
  • Proteoglycans / administration & dosage
  • Proteoglycans / isolation & purification
  • Proteoglycans / metabolism*
  • Rats
  • Rats, Sprague-Dawley
  • Sarcoma, Experimental
  • Stereotaxic Techniques
  • Thiazoles
  • Time Factors

Substances

  • Amyloid beta-Peptides
  • Benzothiazoles
  • Glycosaminoglycans
  • Heparan Sulfate Proteoglycans
  • Proteoglycans
  • Thiazoles
  • perlecan
  • thioflavin T
  • Congo Red
  • Heparitin Sulfate