Nuclear Localization of Ataxin-3 Is Required for the Manifestation of Symptoms in SCA3: In Vivo Evidence
Ulrike Bichelmeier, Thorsten Schmidt, Jeannette Hübener, Jana Boy, Lukas Rüttiger, Karina Häbig, Sven Poths, Michael Bonin, Marlies Knipper, Werner J. Schmidt, Johannes Wilbertz, Hartwig Wolburg, Franco Laccone and Olaf Riess
Journal of Neuroscience 11 July 2007, 27 (28) 7418-7428; DOI: https://doi.org/10.1523/JNEUROSCI.4540-06.2007