Skip to main content
SpringerLink
Log in

Megacystis-microcolon-intestinal hypoperistalsis syndrome in a newborn girl whose brother had prune belly syndrome: Common pathogenesis?

  • Short Reports
  • Published:
Pediatric Radiology Aims and scope Submit manuscript

Abstract

A case of megacystis-microcolon-intestinal hypoperistalsis syndrome (MMIHS) is presented. There were important findings: a urachal remnant and a brother with prune belly syndrome (PBS). After a review of the literature, many common characteristic of MMIHS and PBS are described: flaccid abdomen, dilatation of the urinary tract, intestinal malrotation, cryptorchidism, urachal remnants and familial incidence. MMIHS and PBS may be manifestations of the same underlying process.

This is a preview of subscription content, log in via an institution to check access.

Access this article

Log in via an institution

Price excludes VAT (USA)
Tax calculation will be finalised during checkout.

Instant access to the full article PDF.

Institutional subscriptions

References

  1. Berdon WE, Baker DH, Blanc WA, Gay B, Santulli TV and Donovan C (1976) Megacystis-microcolon-intestinal hypoperistalsis syndrome: a new cause of intestinal obstruction in the newborn. AJR 126: 957

    PubMed  Google Scholar 

  2. Amoury RA, Fellows RA, Goodwin CD, Hall RT, Falder TM and Ashcraft KW (1977) Megacystis-microcolon-intestinal hypoperistalsis syndrome: a cause of intestinal obstruction in the newborn period. J Pediatr Surg 12: 1063

    PubMed  Google Scholar 

  3. Wiswell TE, Rawlings JJ, Wilson JL, Pettett G (1979) Megacystis-microcolon-intestinal hypoperistalsis syndrome. Pediatrics 63: 805

    PubMed  Google Scholar 

  4. Young LW, Yunis EJ, Girdany BR, Sieber WK (1981) Megacystis-microcolon-intestinal hypoperistalsis syndrome: additional clinical, radiologic, surgical and histopathologic aspects. AJR 137: 749

    PubMed  Google Scholar 

  5. Krook PM (1980) Megacystis-microcolon-intestinal hypoperistalsis syndrome in a male infant. Radiology 136: 649

    PubMed  Google Scholar 

  6. Summer T, Crowe J, Klein A, Shaffner LS, Nelson LH, Resnick MI, Weaver RL and Young LW (1981) Megacystis-microcolon-intestinal hypoperistalsis syndrome. Am J Dis Child 135: 67

    PubMed  Google Scholar 

  7. Pagon RA, Smith DW and Shepard TH (1979) Urethral obstruction malformation complex: a cause of abdominal muscle deficiency and the “prune belly”. J Pediatr 94: 900

    PubMed  Google Scholar 

  8. Berdon WE, Baker DH, Wigger HJ, Blanc WA (1977) The radiologic and pathologic spectrum of the prune belly syndrome. Rad Clin North Am 15: 83

    Google Scholar 

  9. Lebowitz RL, Griscom NT (1977) Neonatal hydronephrosis: 146 cases. Rad Clin North Am 15: 49

    Google Scholar 

Download references

Author information

Authors and Affiliations

  1. Department of Radiology, Hospital Infantil N.S. da Glória, Vitória

    G. Oliveira

  2. Department of Radiology, Universidade Federal de Minas Gerais, Belo Horizonte

    Maria I. Boechat

  3. Department of Pediatric Surgery, Hospital Infantil N.S. da Glória, Vitória, Brazil

    M. A. Ferreira

Authors
  1. G. Oliveira
    View author publications

    You can also search for this author in PubMed Google Scholar

  2. Maria I. Boechat
    View author publications

    You can also search for this author in PubMed Google Scholar

  3. M. A. Ferreira
    View author publications

    You can also search for this author in PubMed Google Scholar

Rights and permissions

Reprints and permissions

About this article

Cite this article

Oliveira, G., Boechat, M.I. & Ferreira, M.A. Megacystis-microcolon-intestinal hypoperistalsis syndrome in a newborn girl whose brother had prune belly syndrome: Common pathogenesis?. Pediatr Radiol 13, 294–296 (1983). https://doi.org/10.1007/BF00973353

Download citation

  • Accepted:

  • Issue Date:

  • DOI: https://doi.org/10.1007/BF00973353

Keywords

Search

Navigation